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Nutritional anaemias
(D50D53)
D50
D50.0
D50.1
Sideropenic dysphagia
Kelly-Paterson syndrome
Plummer-Vinson syndrome
D50.8
D50.9
D51
D51.0
Biermer
pernicious (congenital)
Congenital intrinsic factor deficiency
D51.1
Vitamin B12 deficiency anaemia due to selective vitamin B12 malabsorption with
proteinuria
Imerslund(-Grsbeck) syndrome
Megaloblastic hereditary anaemia
D51.2
D51.3
Transcobalamin II deficiency
Other dietary vitamin B12 deficiency anaemia
Vegan anaemia
D51.8
D51.9
D52
D52.0
D52.1
D52.8
D52.9
D53
D53.0
D53.1
D53.2
Scorbutic anaemia
Excludes: scurvy (E54)
D53.8
D53.9
Haemolytic anaemias
(D55D59)
D55
D55.0
D55.1
D55.2
D55.3
D55.8
D55.9
D56
Thalassaemia
D56.0
Alpha thalassaemia
Excludes: hydrops fetalis due to haemolytic disease (P56.-)
D56.1
Beta thalassaemia
Cooley's anaemia
Severe beta thalassaemia
Sickle-cell beta thalassaemia
Thalassaemia:
intermedia
major
D56.2
Delta-beta thalassaemia
D56.3
Thalassaemia trait
D56.4
D56.8
Other thalassaemias
D56.9
Thalassaemia, unspecified
Mediterranean anaemia (with other haemoglobinopathy)
Thalassaemia (minor)(mixed)(with other haemoglobinopathy)
D57
Sickle-cell disorders
Excludes: other haemoglobinopathies (D58.-)
sickle-cell beta thalassaemia (D56.1)
D57.0
D57.1
disease
disorder
D57.2
} NOS
}
D57.3
Sickle-cell trait
Hb-S trait
Heterozygous haemoglobin S
D57.8
D58
D58.0
Hereditary spherocytosis
Acholuric (familial) jaundice
Congenital (spherocytic) haemolytic icterus
Minkowski-Chauffard syndrome
D58.1
Hereditary elliptocytosis
Elliptocytosis (congenital)
Ovalocytosis (congenital)(hereditary)
D58.2
Other haemoglobinopathies
Abnormal haemoglobin NOS
Congenital Heinz body anaemia
Disease:
Hb-C
Hb-D
Hb-E
Haemoglobinopathy NOS
Unstable haemoglobin haemolytic disease
Excludes: familial polycythaemia (D75.0)
Hb-M disease (D74.0)
hereditary persistence of fetal haemoglobin [HPFH] (D56.4)
high-altitude polycythaemia (D75.1)
methaemoglobinaemia (D74.-)
D58.8
D58.9
D59
D59.0
D59.1
D59.2
D59.3
Haemolytic-uraemic syndrome
D59.4
D59.5
D59.6
D59.8
D59.9
D60.0
D60.1
D60.8
D60.9
D61
D61.0
D61.1
D61.2
D61.3
D61.8
D61.9
D62
D63*
D63.0*
D63.8*
D64
Other anaemias
Excludes: refractory anaemia:
NOS (D46.4)
with excess of blasts (D46.2)
with transformation (D46.3)
with sideroblasts (D46.1)
without sideroblasts (D46.0)
D64.0
D64.1
D64.2
D64.3
D64.4
D64.8
D64.9
Anaemia, unspecified
Afibrinogenaemia, acquired
Consumption coagulopathy
Diffuse or disseminated intravascular coagulation [DIC]
Fibrinolytic haemorrhage, acquired
Purpura:
fibrinolytic
fulminans
Excludes: that (complicating):
abortion or ectopic or molar pregnancy (O00O07, O08.1)
in newborn (P60)
pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
D66
D67
D68
D68.0
D68.1
D68.2
D68.3
D68.4
D68.8
D68.9
D69
D69.0
Allergic purpura
Purpura:
anaphylactoid
Henoch(-Schnlein)
nonthrombocytopenic:
haemorrhagic
idiopathic
vascular
Vasculitis, allergic
D69.1
D69.2
D69.3
D69.4
D69.5
Secondary thrombocytopenia
Use additional external cause code (Chapter XX), if desired, to identify cause.
D69.6
Thrombocytopenia, unspecified
D69.8
D69.9
Agranulocytosis
Agranulocytic angina
Infantile genetic agranulocytosis
Kostmann's disease
Neutropenia:
NOS
congenital
cyclic
drug-induced
periodic
splenic (primary)
toxic
Neutropenic splenomegaly
Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.
Excludes: transient neonatal neutropenia (P61.5)
D71
D72
D72.0
D72.1
Eosinophilia
Eosinophilia:
allergic
hereditary
D72.8
D72.9
D73
Diseases of spleen
D73.0
Hyposplenism
Asplenia, postsurgical
Atrophy of spleen
Excludes: asplenia (congenital) (Q89.0)
D73.1
Hypersplenism
Excludes: splenomegaly:
NOS (R16.1)
congenital (Q89.0)
D73.2
D73.3
Abscess of spleen
D73.4
Cyst of spleen
D73.5
Infarction of spleen
Splenic rupture, nontraumatic
Torsion of spleen
Excludes: traumatic rupture of spleen (S36.0)
D73.8
D73.9
D74
Methaemoglobinaemia
D74.0
Congenital methaemoglobinaemia
Congenital NADH-methaemoglobin reductase deficiency
Haemoglobin-M [Hb-M] disease
Methaemoglobinaemia, hereditary
D74.8
Other methaemoglobinaemias
Acquired methaemoglobinaemia (with sulfhaemoglobinaemia)
Toxic methaemoglobinaemia
Use additional external cause code (Chapter XX), if desired, to identify cause.
D74.9
Methaemoglobinaemia, unspecified
D75
NOS (I88.9)
acute (L04.-)
chronic (I88.1)
mesenteric (acute)(chronic) (I88.0)
D75.0
Familial erythrocytosis
Polycythaemia:
benign
familial
Excludes: hereditary ovalocytosis (D58.1)
D75.1
Secondary polycythaemia
Polycythaemia:
acquired
due to:
erythropoietin
fall in plasma volume
high altitude
stress
emotional
hypoxaemic
nephrogenous
relative
Excludes: polycythaemia:
neonatorum (P61.1)
vera (D45)
D75.2
Essential thrombocytosis
Excludes: essential (haemorrhagic) thrombocythaemia (D47.3)
D75.8
D75.9
D76
D76.0
D76.1
Haemophagocytic lymphohistiocytosis
Familial haemophagocytic reticulosis
Histiocytoses of mononuclear phagocytes other than Langerhans' cells NOS
D76.2
D76.3
D77*
D80
D80.0
Hereditary hypogammaglobulinaemia
Autosomal recessive agammaglobulinaemia (Swiss type)
X-linked agammaglobulinaemia [Bruton] (with growth hormone deficiency)
D80.1
Nonfamilial hypogammaglobulinaemia
Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
Common variable agammaglobulinaemia [CVAgamma]
Hypogammaglobulinaemia NOS
D80.2
D80.3
D80.4
D80.5
D80.6
D80.7
D80.8
D80.9
D81
Combined immunodeficiencies
Excludes: autosomal recessive agammaglobulinaemia (Swiss type) (D80.0)
D81.0
D81.1
D81.2
D81.3
D81.4
Nezelof's syndrome
D81.5
D81.6
D81.7
D81.8
D81.9
D82
D82.0
Wiskott-Aldrich syndrome
Immunodeficiency with thrombocytopenia and eczema
D82.1
Di George's syndrome
Pharyngeal pouch syndrome
Thymic:
alymphoplasia
aplasia or hypoplasia with immunodeficiency
D82.2
D82.3
D82.4
D82.8
D82.9
D83
D83.0
D83.1
D83.2
D83.8
D83.9
D84
Other immunodeficiencies
D84.0
D84.1
D84.8
D84.9
Immunodeficiency, unspecified
D86
Sarcoidosis
D86.0
Sarcoidosis of lung
D86.1
D86.2
D86.3
Sarcoidosis of skin
D86.8
D86.9
Sarcoidosis, unspecified
D89
D89.0
Polyclonal hypergammaglobulinaemia
Benign hypergammaglobulinaemic purpura
Polyclonal gammopathy NOS
D89.1
Cryoglobulinaemia
Cryoglobulinaemia:
essential
idiopathic
mixed
primary
secondary
Cryoglobulinaemic:
purpura
vasculitis
D89.2
Hypergammaglobulinaemia, unspecified
D89.8
Other specified disorders involving the immune mechanism, not elsewhere classified
D89.9
Extracted from ICD-10 Second Edition, 2005, Diseases of the blood and bloodforming organs.