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HYPOSPADIAS
Hypo- below, Spadon- orifice
Urethral meatus opens on ventral side of the penis, proximal to the tip of glans penis Incidence ..1/125 to 1/250
EMBRYOLOGY
Cloacal membrane, genital tubercle, labioscrotal swellings Androgen stimulationphallus elongation 3 phases of urethral formation
Posterior urethra formation Anterior urethra formation Glandular segment formation
Prepuce formation
CLASSIFICATION
Smith
Able
..
.. I , II, III degree
Browne .. Coronal - distal penile, proximal penile, penoscrotal, scrotal penile Basrat .. (post chordee release)
CLASSIFICATION (LOCATION)
DISTAL
Glandular, Coronal, Distal penile
MIDPENILE
Midshaft
PROXIMAL
Proximal penile, Penoscrotal, Scrotal, Perineal
PARTS OF HYPOSPADIAS
Meatus usually non-stenotic Stenosis more common in distal hypospadias Megalomeatus intact prepuce
SKIN..
Ventral defect & dorsal hood
Urethral delta
CURVATURE
Skin attachments Bucks defect
Urethral plate
Cavernosa defects Problems of unhealthy urethra
(2/3) (1/3)
TYPE II :
BUCKS & DARTOS DEFECT
TYPE III :
DARTOS & SKIN DEFECT
FEATURES OF REPAIR
Artificial erection ( Gittes & McLaughlin)
Meatal correction Neourethral formation Orthoplasty Skin cover. Dorsal prepuce Time of repair Neourethral cover : Tunica Vaginalis : 6months - 12months
Decrease in hypospadias
Decrease in chordee Increased vascularity Increased corporal thickness both proximal & distal
TREATMENT OPTIONS
GLANDULAR & SUBCORONAL
MAGPI GAP MIP
DISTAL PENILE
MATHEIU SNODGRASS DEVINE HORTAN MUSTARDEE
TREATMENT OPTIONS
MIDPENILE
SNODGRASS ONLAY ISLAND PREPUTIAL FLAP KING HODGSON II
PROXIMAL PENILE
TRANSVERSE PREPUTIAL FLAP HODGSON I HODGSON III
TREATMENT OPTIONS
POSTERIOR URETHRA
TRANSVERSE PREPUTIAL FLAP
TWO STAGED
BUCCAL.TUBULAR.GLANS CHANNEL BAYRS CECIL SMITH
COMPLICATIONS
BLEEDING & HEMATOMA MEATAL STENOSIS URETHROCUTANEOUS INFECTION URETHRAL DIVERTICULA RECURRENT CURVATURE / STRICTURE BREAK DOWN