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Etiologi
DIAGNOSIS
BA can be suspected
if the gallbladder is shrunken despite fasting
if the liver hilum appears exceedingly
hyperechogenic ("triangular chord sign")
if there is a cyst in the liver hilum,
if features of the polysplenia syndrome are
identified: multiples spleens, preduodenal
portal vein, absence of retrohepatic vena cava
Treatment:
The current management of BA patients
involves two steps:
1) in the neonatal period, the Kasai
operation, which aims at restoring a biliary
flow to the intestine.
2) subsequent liver transplantation in case
of failure of the Kasai operation to restore
the biliary flow and/or complications of the
biliary cirrhosis